Study Status: Recruiting
Recruit Status: Recruiting
Study Type: Interventional
Official Title: Bilateral Orthotopic Lung Transplant in Tandem With CD3+ and CD19+ Cell Depleted Bone Marrow Transplant From Partially HLA-Matched Cadaveric Donors
Brief Summary: The purpose of this study is to determine whether bilateral orthotopic lung transplantation (BOLT) followed by cadaveric partially-matched hematopoietic stem cell transplantation (HSCT) is safe and effective for patients aged 5-40 years with primary immunodeficiency (PID) and end-stage lung disease.