Limited scleroderma, or CREST syndrome, is one subtype of scleroderma — a condition that literally means "hardened skin."
The skin changes associated with limited scleroderma typically occur only in the lower arms and legs and sometimes the face and throat. Limited scleroderma can also affect your digestive tract.
The problems caused by limited scleroderma may be minor. Sometimes, however, the disease affects the lungs or heart, with potentially serious results. Limited scleroderma has no known cure, and treatments focus on managing symptoms and preventing serious complications.
Source: http://www.mayoclinic.com
While some varieties of scleroderma occur rapidly, signs and symptoms of limited scleroderma usually develop gradually. They include:
Source: http://www.mayoclinic.com
Limited scleroderma is believed to be an autoimmune disorder — one in which your immune system turns against your own body. In limited scleroderma, the immune system appears to stimulate the production of too much collagen, a key component of connective tissue. This overproduction of collagen builds up in the skin and internal organs, impairing their function.
Source: http://www.mayoclinic.com
Like other unusual and complex autoimmune disorders, limited scleroderma can be difficult to diagnose. Signs and symptoms vary widely and often resemble those of other diseases. To complicate matters even more, limited scleroderma sometimes occurs with other autoimmune conditions — such as polymyositis, lupus and rheumatoid arthritis.
The diagnosis of limited scleroderma is generally made based on your signs and symptoms. In addition, tests that may help in the diagnosis of limited scleroderma include:
In addition to tests that may help diagnose limited scleroderma itself, your doctor may recommend additional tests to identify any lung, heart or gastrointestinal complications.
Source: http://www.mayoclinic.com
The visible signs of limited scleroderma — tight, thick skin on your fingers, hands and face — can affect the way you feel about your appearance; make everyday tasks, such as opening a jar or shaving, more difficult; and even affect your speech. But the most serious complications tend to occur beneath your skin.
Source: http://www.mayoclinic.com
To help boost blood flow to extremities, you might try biofeedback, a technique that teaches you to control certain body responses. Relaxation exercises or medication also may be helpful.
Source: http://www.mayoclinic.com
To reduce Raynaud's symptoms, wear gloves or mittens outdoors when the weather is cool and indoors when you reach into the freezer. To maintain your body's core temperature when it's cool, dress in layers and wear a hat or scarf, thermal socks, and well-fitting boots or shoes that don't cut off your circulation.
If you smoke, talk to your doctor about the best ways to quit. Nicotine constricts your blood vessels, making Raynaud's phenomenon worse. Smoking also worsens heartburn.
Regular exercise can help you maintain your flexibility and strength. Ask your doctor or physical or occupational therapist what activities are right for you.
If you have difficulty swallowing, choose soft, moist foods and chew them well. To minimize acid reflux:
Excess collagen destroys sweat and oil glands, leaving your skin stiff and dry. To help soften your skin:
Be sure to have regular checkups and use any special rinses or toothpastes your dentist recommends. If your mouth is chronically dry, try drinking more water and sucking on ice chips or hard, sugarless candy. When these measures fail, your dentist may prescribe a medication to stimulate the flow of saliva.
Source: http://www.mayoclinic.com
Because limited scleroderma can affect your appearance and your ability to perform simple tasks, your self-esteem may suffer. It's common for people with limited scleroderma to become depressed.
Talking with a counselor may help you come to grips with the changes caused by this disease. Communicating with people facing the same illness, either through online or in-person support groups, also may be helpful.
Source: http://www.mayoclinic.com
Source: http://www.mayoclinic.com
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