Overview

Desmoplastic (des-moe-PLAS-tik) small round cell tumors are a type of soft tissue cancer that typically begins in the abdomen. Rarely, this type of cancer can occur in other parts of the body.

Desmoplastic small round cell tumors occur most often in young men and boys, though they can occur at any age and can also affect women.

These aggressive cancers often form as multiple tumors in the tissue (peritoneum) that lines the inside of the abdomen and pelvis. They quickly spread to other structures within the abdomen.

Desmoplastic small round cell tumors are a type of soft tissue sarcoma.

Treatment for desmoplastic small round cell tumors typically involves a combination of treatments, such as surgery, chemotherapy and radiation therapy.